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« BAV congénital » : différence entre les versions

722 octets ajoutés ,  4 avril 2023
aucun résumé des modifications
Aucun résumé des modifications
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Les formes découvertes plus tardivement, plusieurs semaines après la naissance, sont génaralement de melleur pronostic.
Les formes découvertes plus tardivement, plusieurs semaines après la naissance, sont génaralement de melleur pronostic.
En cas de BAV congénital idiopathique, on retrouve 70% de BAV complet au diagnostic, avec un échappement à QRS fins dans 70% des cas. 85% des patients sont asymptomatiques lors du diagnostic initial.


ECG d'un BAV congénital immun chez un nouveau-né :
ECG d'un BAV congénital immun chez un nouveau-né :
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<ref>Balmer C, Fasnacht M, Rahn M, Molinari L, Bauersfeld U. Long-term follow up of children with congenital complete atrioventricular block and the impact of pacemaker therapy. Europace. oct 2002;4(4):345‑9.</ref><ref>Baruteau AE, Pass RH, Thambo JB, Behaghel A, Le Pennec S, Perdreau E, et al. Congenital and childhood atrioventricular blocks: pathophysiology and contemporary management. Eur J Pediatr. sept 2016;175(9):1235‑48.</ref><ref>Breur JMPJ, Kapusta L, Stoutenbeek P, Visser GHA, van den Berg P, Meijboom EJ. Isolated congenital atrioventricular block diagnosed in utero: natural history and outcome. J Matern Fetal Neonatal Med. juill 2008;21(7):469‑76.</ref><ref>Hunter LE, Simpson JM. Atrioventricular block during fetal life. J Saudi Heart Assoc. 2015 Jul;27(3):164-78. doi: 10.1016/j.jsha.2014.07.001. Epub 2014 Jul 10. PMID: 26136631; PMCID: PMC4481419.</ref><ref>Gozar L, Marginean C, Fagarasan A, Muntean I, Cerghit-Paler A, Miklosi D, Toganel R. Congenital complete atrioventricular block from literature to clinical approach - a case series and literature review. Med Ultrason. 2021 May 20;23(2):188-193. doi: 10.11152/mu-2723. Epub 2020 Dec 5. PMID: 33626113.</ref><ref>Writing Committee Members; Shah MJ, Silka MJ, Silva JNA, Balaji S, Beach CM, Benjamin MN, Berul CI, Cannon B, Cecchin F, Cohen MI, Dalal AS, Dechert BE, Foster A, Gebauer R, Gonzalez Corcia MC, Kannankeril PJ, Karpawich PP, Kim JJ, Krishna MR, Kubuš P, LaPage MJ, Mah DY, Malloy-Walton L, Miyazaki A, Motonaga KS, Niu MC, Olen M, Paul T, Rosenthal E, Saarel EV, Silvetti MS, Stephenson EA, Tan RB, Triedman J, Bergen NHV, Wackel PL. 2021 PACES Expert Consensus Statement on the Indications and Management of Cardiovascular Implantable Electronic Devices in Pediatric Patients. Heart Rhythm. 2021 Nov;18(11):1888-1924. doi: 10.1016/j.hrthm.2021.07.038. Epub 2021 Jul 29. PMID: 34363988.</ref><ref>Lupoglazoff JM, Cheav T, Baroudi G, Berthet M, Denjoy I, Cauchemez B, Extramiana F, Chahine M, Guicheney P. Homozygous SCN5A mutation in long-QT syndrome with functional two-to-one atrioventricular block. Circ Res. 2001 Jul 20;89(2):E16-21. doi: 10.1161/hh1401.095087. PMID: 11463728.</ref>
<ref>Balmer C, Fasnacht M, Rahn M, Molinari L, Bauersfeld U. Long-term follow up of children with congenital complete atrioventricular block and the impact of pacemaker therapy. Europace. oct 2002;4(4):345‑9.</ref><ref>Baruteau AE, Pass RH, Thambo JB, Behaghel A, Le Pennec S, Perdreau E, et al. Congenital and childhood atrioventricular blocks: pathophysiology and contemporary management. Eur J Pediatr. sept 2016;175(9):1235‑48.</ref><ref>Breur JMPJ, Kapusta L, Stoutenbeek P, Visser GHA, van den Berg P, Meijboom EJ. Isolated congenital atrioventricular block diagnosed in utero: natural history and outcome. J Matern Fetal Neonatal Med. juill 2008;21(7):469‑76.</ref><ref>Hunter LE, Simpson JM. Atrioventricular block during fetal life. J Saudi Heart Assoc. 2015 Jul;27(3):164-78. doi: 10.1016/j.jsha.2014.07.001. Epub 2014 Jul 10. PMID: 26136631; PMCID: PMC4481419.</ref><ref>Gozar L, Marginean C, Fagarasan A, Muntean I, Cerghit-Paler A, Miklosi D, Toganel R. Congenital complete atrioventricular block from literature to clinical approach - a case series and literature review. Med Ultrason. 2021 May 20;23(2):188-193. doi: 10.11152/mu-2723. Epub 2020 Dec 5. PMID: 33626113.</ref><ref>Writing Committee Members; Shah MJ, Silka MJ, Silva JNA, Balaji S, Beach CM, Benjamin MN, Berul CI, Cannon B, Cecchin F, Cohen MI, Dalal AS, Dechert BE, Foster A, Gebauer R, Gonzalez Corcia MC, Kannankeril PJ, Karpawich PP, Kim JJ, Krishna MR, Kubuš P, LaPage MJ, Mah DY, Malloy-Walton L, Miyazaki A, Motonaga KS, Niu MC, Olen M, Paul T, Rosenthal E, Saarel EV, Silvetti MS, Stephenson EA, Tan RB, Triedman J, Bergen NHV, Wackel PL. 2021 PACES Expert Consensus Statement on the Indications and Management of Cardiovascular Implantable Electronic Devices in Pediatric Patients. Heart Rhythm. 2021 Nov;18(11):1888-1924. doi: 10.1016/j.hrthm.2021.07.038. Epub 2021 Jul 29. PMID: 34363988.</ref><ref>Lupoglazoff JM, Cheav T, Baroudi G, Berthet M, Denjoy I, Cauchemez B, Extramiana F, Chahine M, Guicheney P. Homozygous SCN5A mutation in long-QT syndrome with functional two-to-one atrioventricular block. Circ Res. 2001 Jul 20;89(2):E16-21. doi: 10.1161/hh1401.095087. PMID: 11463728.</ref>
<references /><ref>Baruteau AE, Fouchard S, Behaghel A, Mabo P, Villain E, Thambo JB, Marçon F, Gournay V, Rouault F, Chantepie A, Guillaumont S, Godart F, Bonnet C, Fraisse A, Schleich JM, Lusson JR, Dulac Y, Leclercq C, Daubert JC, Schott JJ, Le Marec H, Probst V. Characteristics and long-term outcome of non-immune isolated atrioventricular block diagnosed in utero or early childhood: a multicentre study. Eur Heart J. 2012 Mar;33(5):622-9. doi: 10.1093/eurheartj/ehr347. Epub 2011 Sep 14. PMID: 21920962.</ref>
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